Thin Glomerular basement membrane disease, also called benign recurrent hematuria is characterized by diffuse thinning of the glomerular basement membrane, hematuria, and nonprogressive nephropathy clinically and is frequently familial. The
incidence of
this disease is unknown, but recently published reports show comparatively common & similar to that of idiopathic IgA nephropathy14,k15,27). But the published reports on this case are rather scarce, especially in adults.
The hallmark of this condition is diffuse thinning of glomerular basement membrane on electron microscopy without any deposition of immunoglobulins and complements.
The exact incidence, pathogenesis and prognosis are not yet to be determined.
We experienced 2 cases of thin glomerular basement membrane disease. So, we report these cases with brief review of the literature.
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